Portal hypertension resulting from non-cirrhotic extrahepatic portal vein obstruction is a cause of severe morbidity related to variceal bleeding in children. In patients not eligible for Meso-Rex bypass, rescue interventions for refractory variceal bleeding have traditionally included surgical porto-systemic shunts or transjugular intrahepatic porto-systemic shunt (TIPS), which alter the normal physiology of liver perfusion and expose children to long-term complications. Portal vein recanalization is a recently described technique which aims to restore the hepatopetal flow through the native portal system but its feasibility is often limited. We aim to present two innovative techniques of percutaneous non-anatomical portal vein recanalization for treating non-cirrhotic extrahepatic portal vein obstruction in children who failed anatomical revascularization.

Martins De Mattos, K., Marra, P., Carbone, F., Muglia, R., Dulcetta, L., Fagiuoli, S., et al. (2025). Non-anatomical revascularization of the portal vein in children with non-cirrhotic extrahepatic portal vein obstruction. PEDIATRIC RADIOLOGY, 55(6), 1308-1312 [10.1007/s00247-025-06218-1].

Non-anatomical revascularization of the portal vein in children with non-cirrhotic extrahepatic portal vein obstruction

Martins de Mattos K. D.;Marra P.;Carbone F. S.;Dulcetta L.;Fagiuoli S.;D'Antiga L.;Sironi S.
2025

Abstract

Portal hypertension resulting from non-cirrhotic extrahepatic portal vein obstruction is a cause of severe morbidity related to variceal bleeding in children. In patients not eligible for Meso-Rex bypass, rescue interventions for refractory variceal bleeding have traditionally included surgical porto-systemic shunts or transjugular intrahepatic porto-systemic shunt (TIPS), which alter the normal physiology of liver perfusion and expose children to long-term complications. Portal vein recanalization is a recently described technique which aims to restore the hepatopetal flow through the native portal system but its feasibility is often limited. We aim to present two innovative techniques of percutaneous non-anatomical portal vein recanalization for treating non-cirrhotic extrahepatic portal vein obstruction in children who failed anatomical revascularization.
Articolo in rivista - Articolo scientifico
Angioplasty; Cavernous transformation; Endovascular procedures; Portal hypertension; Portal vein;
English
19-mar-2025
2025
55
6
1308
1312
100511
none
Martins De Mattos, K., Marra, P., Carbone, F., Muglia, R., Dulcetta, L., Fagiuoli, S., et al. (2025). Non-anatomical revascularization of the portal vein in children with non-cirrhotic extrahepatic portal vein obstruction. PEDIATRIC RADIOLOGY, 55(6), 1308-1312 [10.1007/s00247-025-06218-1].
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/10281/553121
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