Hereditary Hemorrhagic Telangiectasia or Rendu-Osler-Weber syndrome is an incomplete penetrance dominant autosomal transmission disease which determines microcirculatory beds alterations (capillary and venules), caused by the loss of the support tissues that usually enclose blood vessels, and hemorrhage potentially in every organ. The syndrome clinical manifestations are multiple telangiectasia of small proportions on the skin or on the mucous membranes (e.g. of the gastrointestinal tract or other organs), in association with recurring bleedings of the affected areas and external and internal melena. The treatment is a supportive one so to prevent complications. This study reports a case of a patient affected by this syndrome in need of a dental implant following the fracture of a tooth. Furthermore, a bibliographical review of etiopathogenesis, clinical manifestations and therapy options has been made.

Leonida, A., Caccianiga, G., Lauritano, D., Longoni, S., Ceraulo, S., Baldoni, M. (2019). Intra and extra oral clinical manifestations of Rendu-Osler-Weber syndrome: case report and literature review. JOURNAL OF BIOLOGICAL REGULATORS & HOMEOSTATIC AGENTS, 33(6), 49-58.

Intra and extra oral clinical manifestations of Rendu-Osler-Weber syndrome: case report and literature review

Caccianiga, G
Secondo
;
Lauritano, D;Ceraulo, S;Baldoni, M
Ultimo
2019

Abstract

Hereditary Hemorrhagic Telangiectasia or Rendu-Osler-Weber syndrome is an incomplete penetrance dominant autosomal transmission disease which determines microcirculatory beds alterations (capillary and venules), caused by the loss of the support tissues that usually enclose blood vessels, and hemorrhage potentially in every organ. The syndrome clinical manifestations are multiple telangiectasia of small proportions on the skin or on the mucous membranes (e.g. of the gastrointestinal tract or other organs), in association with recurring bleedings of the affected areas and external and internal melena. The treatment is a supportive one so to prevent complications. This study reports a case of a patient affected by this syndrome in need of a dental implant following the fracture of a tooth. Furthermore, a bibliographical review of etiopathogenesis, clinical manifestations and therapy options has been made.
Articolo in rivista - Articolo scientifico
Hereditary hemorrhagic telangiectasia; Oral medicine; Oral mucosa; Rendu-Osler-Weber syndrome;
English
2019
33
6
49
58
reserved
Leonida, A., Caccianiga, G., Lauritano, D., Longoni, S., Ceraulo, S., Baldoni, M. (2019). Intra and extra oral clinical manifestations of Rendu-Osler-Weber syndrome: case report and literature review. JOURNAL OF BIOLOGICAL REGULATORS & HOMEOSTATIC AGENTS, 33(6), 49-58.
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/10281/257131
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