We describe the case of a 17-year-old Hispanic boy who had had erythroderma and diffuse lymphadenopathy for approximately 6 months. A diagnosis of Sézary syndrome was made on the basis of the histologic features of the skin; the presence of the same T-cell clone on the skin, blood, and bone marrow; and the high CD4+ lymphocyte count with an aberrant phenotype in peripheral blood; bone marrow involvement was also present. The patient was treated with systemic gemcitabine and achieved partial remission.
Alberti-Violetti, S., Vezzoli, P., Corti, L., Fanoni, D., Merlo, V., Venegoni, L., et al. (2016). Sézary Syndrome in a 17-Year-Old Boy: Clinicopathologic Features and Genomic Profile. PEDIATRIC DERMATOLOGY, 33(5), e318-e321.
Citazione: | Alberti-Violetti, S., Vezzoli, P., Corti, L., Fanoni, D., Merlo, V., Venegoni, L., et al. (2016). Sézary Syndrome in a 17-Year-Old Boy: Clinicopathologic Features and Genomic Profile. PEDIATRIC DERMATOLOGY, 33(5), e318-e321. |
Tipo: | Articolo in rivista - Articolo scientifico |
Carattere della pubblicazione: | Scientifica |
Presenza di un coautore afferente ad Istituzioni straniere: | No |
Titolo: | Sézary Syndrome in a 17-Year-Old Boy: Clinicopathologic Features and Genomic Profile |
Autori: | Alberti-Violetti, S; Vezzoli, P; Corti, L; Fanoni, D; Merlo, V; Venegoni, L; Reseghetti, A; Berti, E |
Autori: | BERTI, EMILIO (Ultimo) |
Data di pubblicazione: | 2016 |
Lingua: | English |
Rivista: | PEDIATRIC DERMATOLOGY |
Digital Object Identifier (DOI): | http://dx.doi.org/10.1111/pde.12930 |
Appare nelle tipologie: | 01 - Articolo su rivista |